Mondini dysplasia and cochlear implantation
Reviewed by Yovina Khiroya-Morjaria

Approximately 20-28% of sensorineural hearing loss in children arises due to a cochlear malformation. Mondini dysplasia includes a cochlear with one and a half turns and an incomplete interscalar septum. Cochlear implantation is a common treatment protocol for children with inner ear malformations. This comparative study aimed to investigate the development of speech skills in children with Mondini dysplasia who have been implanted. The team compared speech score results between 23 children with cochlear implant that had ‘incomplete partition type 2’ and 35 cochlear implanted children with no inner ear malformation as a control group. The results of all speech tests were the same across both groups, aside from the speech-in-noise test. The scores of children with Mondini dysplasia were significantly lower for speech in noise in comparison to the control group. The results of this study were found to be consistent with other similar studies assessing cochlear implantation on children with inner ear malformations. Overall, the authors concluded cochlear implantation on children with Mondini dysplasia can be associated with successful outcomes.

Speech perception in noise by children with Mondini dysplasia who had undergone cochlear implantation.
Saeedia M, Alvandimanesh M, Hasanalifard M, et al.
HEARING, BALANCE AND COMMUNICATION
2023;21(4):329–34.